Malformation of tricuspid valve and right ventricle
Leads to tricuspid regurgitation, right ventricular failure and arrhythmias
Range from serious presentation at birth or asymptomatic depending upon severity of tricuspid regurgitation
Rare: 1/20,000 births
Associated with Wolf Parkinson White (WPW)
Diagnostic criteria:
ECHO: tricuspid regurgitation +
History:
Examination:
Investigations
ECG:
RBBB
Delta waves from accessory pathway
Differentials
Movement towards early surgical correction
Ebstein Anomaly and Malformation - StatPearls - NCBI Bookshelf (nih.gov)
ZerotoFinals: https://www.youtube.com/watch?v=Z66ciQPtbO8
Page written in 2024.