Exam Cram

• Histiocytosis X (Langerhans cell histiocytosis) is a rare interstitial lung disease caused by smoking

• Presentation: shortness of breath subacute in young smoker

• CT-Thorax: upper zone bilateral nodules and reticulonodular infiltrates, progressing to cysts

• Management: smoking cessation (resolution in one third), corticosteroids and cytoxics

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